It is with great excitement to announce that the Sjögren’s Foundation, in partnership with the American College of Rheumatology, has led a successful effort to revise the U.S. ICD-10 code for Sjögren’s – a major victory for the Sjögren’s community. As of October 1, 2021, changes are now live and include revisions to the M35.0 and M35.00-M35.04 codes as well as new individual codes to describe additional manifestations of the disease.
The initiative to revise and update the ICD-10 Code for Sjögren’s first began in 2017. Prior to this effort, the code for Sjögren’s fell under the heading for ‘sicca.’ We, and many others knew that Sjögren’s and sicca are not synonymous, with sicca being a symptom but not a disease, and Sjögren’s being a distinct systemic autoimmune rheumatic disease that can affect multiple organs and body systems. While dryness (sicca) certainly occurs in Sjögren’s, dryness alone does not represent the disease and its many other manifestations.
Multiple years of planning and presenting to government agencies has resulted in a revised ICD-10 code for Sjögren’s. The below table details the updates and revisions that have taken place: