An initiative to revise and update the ICD-10 Code for Sjögren’s, which began in 2017, was coordinated and led by the Sjögren’s Foundation, in partnership with the American College of Rheumatology and with the help and input from a group of multi-specialty experts.
Prior to this effort, the code for Sjögren’s fell under the heading for ‘sicca.’ We, and many others knew that Sjögren’s and sicca are not synonymous, with sicca being a symptom but not a disease, and Sjögren’s being a distinct systemic autoimmune rheumatic disease that can affect multiple organs and body systems. While dryness (sicca) certainly occurs in Sjögren’s, dryness alone does not represent the disease and its many other manifestations.
Multiple years of planning and presenting to government agencies has resulted in a revised ICD-10 code for Sjögren’s, which is set to take effect in October 2020. The below table details the updates and revisions that are set to take place.